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RNA interference Glucocorticoids Exercise Myotonic dystrophy Therapy Central nervous system Brain dysfunction Transcriptomics Animals Intermediate filament Mice Transgenic mouse Myotonic Dystrophy Type 1 Mouse models Glucocorticoid-receptor Astrocyte Myelin BIOLOGIE MOLECULAIRE Neuron Muscle GSK3␤ Trinucleotide repeat expansion Endurance training DMPK Cell model Dystrophie Myotonique Quantitative microdialysis Thérapie génique Cell culture model RNA splicing CTG repeats Brain Desmin Mouse model Trinucleotide Repeat Expansion MBNL Gene Therapy Long read sequencing AAV ARN Acetylcholinesterase knockout mouse PCR CTG repeat instability Diaphragm Myotonic dystrophy mouse models Cell penetrating peptide Autophagy Dynamin 2 Myotonic Dystrophy type 1 Motoneuron Heart failure Hypoxia Centronuclear myopathy Gene editing Genotype phenotype correlation ACETYLCHOLINESTERASE Transgenic mouse model Myotonic dystrophy type 1 PacBio Glial cells CRISPR/Cas9 Glutamate Acetylcholinesterase deficiency DMSXL mice CRISPRi Antisense oligonucleotides CMS Alternative splicing Cultured CTG repeat contractions Acute coronary syndrome Dystrophin Male Dystrophie myotonique Heart Duchenne muscular dystrophy Skeletal muscle Oligodendrocytes GABA Aging KNOCKOUT MICE Cells Exercice CONGENITAL MYATHENIC SYNDROME Expression Maximal force Gene therapy Antisense oligonucleotide DM1 RNA biology Astrocytes Myostatin Oligodendrocyte Cytoskeleton Dilated cardiomyopathy Humans Myotonic Dystrophy Muscular dystrophy Cardiac muscle Fibrosis